乳齒第二類型牙本質形成不良—病例報告

Dentinogenesis Imperfecta Type II in Primary Dentition –Case Report

項文宣(Wen-Hsuan Hsiang) ； 張家豪(Chia-Hoa Chang)

《中華牙醫學雜誌》 22卷4期 (2003/12) Pp. 389-398

摘要

第二類型牙本質形成不良（Dentinogenesis imperfecta type II, DI type II），為一種自體顯性遺傳疾病，牙齒會呈現褐色，乳或透明光澤，牙釉質容易碎成小片而喪失，導致其下鈣化不良的牙棖質會快速地咬耗。本病例為一三歲男性幼童，其牙齒成灰褐色透明樣，根尖片顯示出髓腔鈣化、變小，根管狹窄、閉鎖，鈣化異常等現象，且經由病理組織切片、手腳長骨之放射線檢查佐證此診斷; 我們以複合樹脂，不銹鋼牙冠，可徹式空間維持器等重建其齒列，其中以不銹鋼牙冠來保護乳臼齒，對於預後及防止齒質持續剝落磨損，可得到較好的結果。

關鍵字

牙本質形成不良 ； 咬耗 ； 治療

並列摘要

Dentinogenesis imperfecta (DI) type II is a disease inherited in a simple autosomal-dominant mode. The color of the teeth may range from gray to brown with a translucent or opalescent hue. The enamel often chips and fractures away, allowing speedy attrition of the remaining, poorly calcified and softened dentin. This 3-year-old male child suffered impaired esthetics because of his grayish-brown teeth. After checking the roentgenographic and histologic features, DI type II was diagnosed. Then he received treatment with composite resin fillings, stainless steel crowns, and removable space maintainers. Treatment by covering the primary molars with stainless steel crowns showed a good prognosis.

並列關鍵字

dentinogenesis imperfecta ； attrition ； treatment