摘要
病人是一出生18天大的早産男性嬰兒，懷孕期8個月，出生時體重爲2.3kg。病人出生時全身被一層具有光澤的膠膜覆蓋住，同時有眼瞼及嘴唇外翻的現象。此膠膜在出生6到7日開始脫落，接著出現紅斑，脫屑及角化現象，一般實驗室檢查及染色體檢查均爲正常。皮膚組織病理檢查呈現角化過度，顆粒層大部分爲正常但部分呈現增層。病人在出生後4週左右，膠膜完全脫落；紅斑，脫屑則仍持續存在。2到3個月後出現黑褐色的魚鱗癬。本病例的臨床可以主是典型的層狀魚鱗癬，本症極爲罕見。本報告除敘述本病的臨床變化外並論述本症與膠膜兒的關係。
關鍵字
無資料並列摘要
A 18-day-old premature male baby was born to a G3P3 mother with the gestation age of 8 months. His birth weight was 23kg. He was found to have a shiny membrane covering his body at birth. Ectropion and eclabium were also noted. Seven days later, the membrane began to shed, then an underlying erythema, scales and hyperkeratosis were found. At the age of four weeks, the membrane shed completely, but the erythema and desquamation have still persisted. Two to three months later, the ichthyosis was noticed. Consanguinity was noted in this patient's family. Laboratory and chromosome studies were normal. Dermatohistology showed hyperkeratosis and focal hypergranulosis. We reported this typical case of lamellar ichthyosis and discussed the relation-ship between the collodion baby and lamellar ichthyosis.