- 期刊
Moyamoya Disease Manifested Initially by Repeated Attacks of Adversive Seizure: Report of One Case
以轉頭癲癇重覆發作為初發表現之Moyamoya病：一病例報告
摘要
Moyamoya疾病是一種日本人常見的腦血管進行性阻塞病變，而好發的年齡層有二，其一為30至40歲，其二則為10歲以下，但是在日本以外的地區則少有兒童病例被報告。中國人的病例報告僅有五篇，而其中只有14%的年齡低於20歲，我們報告一例以轉頭癲癇重覆發作達一年為初發表現的患者，在腦血管攝影中可見典型之“煙霧狀”側枝循環。頭部電腦斷層攝影可見右額顳部血管阻塞性變化：癲癇發作在moyamoya疾病中的出現比例在日本人為10%，而以癲癇為初發表現的則只有6%，以長達一年的重覆癲癇發作為始而後才出現中風的兒童例尚未曾出現在中國人的病例報告之中，本例經過兩次“腦－硬腦膜－血管接合術”及“腦－肌肉－血管接合術”的手術後情況穩定，同時接合的血管均由血管攝影術證明血流暢順，其臨床上之中風則在手術之後完全恢復。
關鍵字
無資料並列摘要
A nine-year-old Chinese boy had suffered from recurrent episodes of adversive seizure for aboutr a year, seizures which affected the left upper limb, with his head and eyes turning toward the left. An acute attack of left upper-limb weakness and central-type facial palsy occurred before his consultation. Cranial computed tomography (CT) revealed infarction of the right frontoparietal area, and increased density in the head of the left caudate nucleus. Cerebral angiographic study demonstrated a typical pattern of moyamoya disease with bilateral stenosis of the supraclinoid portion of internal carotid arteries. Encephaloduroarteriosynangiosis with encephalomyosynangiosis were performed twice, with resulting good patency of blood flow observed in the follow-up angiographic study.