- 期刊
Scimitar Syndrome Complicated with Right Pneumonectomy Syndrome: Report of One Case
阿拉伯彎刀症候群合併右肺切除症候群：一病例報告
摘要
阿拉伯彎刀症候群爲一先天性疾病包括右肺發育不良，心臟右移，右肺靜脈回流至下腔靜脈及異常腹部主動脈分支灌流至右肺基部等異常。此病因右肺靜脈會合成一巨大靜脈且在胸部放射腺攝影上呈現一阿拉伯彎刀(Scimitar)影像而得名。本病例爲一兩個月大女嬰，因呼吸困難轉診本院，心導管檢查證實爲此病。病嬰四個月大時作右全肺切除。此後，因心臟及縱隔諸器官極度右移造成呼吸道壓迫，二氧化碳蓄積等（右肺切除症候群），病童必須仰賴呼吸器之治療。經過二年半的支持性治療，病童終於可脫離呼吸器自由生活。
關鍵字
無資料並列摘要
A 2-month-old infant, suffering from respiratory distress, was suspected to have scimitar syndrome from a chest roentgeno gram and was diagnosed by cardiac catheterization. Ligation of the aberrant feeding arteries and right lung resection was performed at three and four months of age, respectively. However, the postoperative course was complicated with right pneumonectomy syndrome requiring continuous artificial ventilation. With supportive management, the patient improved gradually and was eventually weaned off the ventilator at three years of age.