Left Multicystic Dysplastic Kidney with Contralateral Ureteropelvic Obstruction: Report of One Case

左側多囊性發育不良腎臓（MCDK）合併對側輸尿管腎盂阻塞：一病例報告

翁根本(Ken-Pen Weng) ； 邱益煊(Yee-Hsuan Chio) ； 黃原逸(Yuan-Yi Huang) ； 宋秉洸(Ping-Kung Sung) ； 謝凱生(Kai-Sheng Hsieh) ； 鍾全生(Choun-Seng Choong)

《Acta Paediatrica Sinica》 39卷5期 (1998/10) Pp. 339-341

https://doi.org/10.7097/APS.199810.0339

摘要

多囊性發育不良腎臓(MCDK)是新生兒常見的腹部腫瘤之一，這種疾病可合併對側腎臓異常，如輸尿管腎盂阻塞等，由於多囔性發育不良腎臓(MCDK)是沒有功能的，仔細評估對側腎臓情況就非常重要，如果對側腎臓有嚴重性阻塞就應立即治療，以保持腎功能，並避免危及生命，我們報告一新生兒病例，産前即知有左側囊狀腎和右側水腎，産後24小時仍呈現無尿情況，經緊急檢查，證實是左側多囊性發育不良腎臓(MCDK)合併對側輸尿管腎孟連接處阻塞，給予妥善治療後，才避免危及生命，特此提出報告，並回顧相關文獻。

關鍵字

多囊性發育不良腎臓 ； 輸尿管腎盂阻塞 ； 無尿

並列摘要

Multicystic dysplastic kidney (MCDK) is a common cause of abdominal mass in neonates. It is frequently associated with malformation of the contralateral kidney, such as ureteropelvic obstruction, etc. Because MCDK is usually functionless, it is important to evaluate the condition of the contralateral kidney. The presence of severe obstruction in the contralateral ureteropelvic junction is life-threatening and prompt treatment should be made to preserve the remaining renal function. We report on a neonate with left MCDK and contralateral ureteropelvic obstruction, presenting as anuria after birth, and also we review the literature.

並列關鍵字

multicystic dysplastic kidney ； ureteropelvic obstruction ； anuria