Gastroschisis: Report of One Case

腹裂畸形症－附病例報告

吳建忠(J. J. Wu) ； 沈國樑(K. L. Shen)

《Journal of Medical Sciences》 1卷3期 (1976/02) Pp. 255-258

摘要

腹裂畸形症是一種極罕見的先天性疾病。此症與臍膨出症在胚胎學上不同處在於與臍無關，其腹裂處常立於臍之側方。此症常伴同其他先天性異常存在。若是內臟突出物不多，且腹腔夠大的話，則可施行初期縫合修補術。否則應使用「加強性達克龍修補袋」並分段縫合修補之。腹裂畸形症之手術死已率約為20%至35%。最常見之死亡原因為敗血症。本文並報告一個腹裂畸形症之病例，經施行初期縫合手術後，結果良好。

並列摘要

A case of gastroschisis has been presented. The embryology, pathology, operative management and postoperative care have been reviewed. Gastroschisis is a very rare congential disease. It differs embryolgoically from omphalocele in that it is an abdominal wall defect lateral to the umbilicus, not involving the umbilicus itself. It frequently is associated with intestinal atresia, imcomplete rotation of gut and multiple abnormalities. Most of the patients can be treated by primary closure. If the abdominal cavity is too small to allow the primary closure, staged closure with the use of Dacron-reinforced silastic prosthesis is preferred. The mortality rate is about 20-35%. The most common cause of death is sepsis.