冠狀動脈異常源出於肺動脈乃-罕見之先天性心臟疾病,其床表徵常使嬰幼兒發生局部心肌缺氧或梗塞,造成心臟衰竭,而導致嬰幼兒之死亡。此疾病之非侵犯性檢查通常是困難而不確定的,而傳統心導管檢查,其侵犯性又易造成嬰幼兒進一步的傷害。 本病例報告乃敘述一個二唬月大的女嬰,其床症狀為擴張性心臟衰竭,而藉著杜卜勒心臟超音波檢查,在手術前正確的診斷出其「左主冠狀動脈異常源出於肺動脈」。本病例所表現之「純舒張期杜卜勒波形」,更是未曾於其它文獻所提及。
The anomalous origin of a coronary artery from the pulmonary trunk is usually difficult to diagnose using crass-sectional echocardiography. This report describes the color and pulsed Doppler echocardiographic features that may be of great help in diagnosing the anomalous origin of the left main coronary artery from the pulmonary trunk, especially in small and critically-ill infants.