先天性腦畸形可以分為器官形成障礙及組織形成障礙兩種。胼胝體形成不良是屬於器官形成障礙中的閉合障礙,是電腦斷層檢查先天性腦畸形異常病變中最常見的一種。單純的胼胝體形成不良在電腦斷層影像上之主要表徵包括下列各項:(1)兩側側腦室呈平行狀且間距加寬。(2)側腦室額角呈蝙蝠翼或牛角狀。(3)兩側側腦室擴大,尤其是枕角部位。(4)腦室間孔變大。(5)第三腦室比正常位置高而且呈不同程度擴大。(6)大腦半球間裂變寬且非常靠近第三腦室。馬偕紀念醫院自民國七十三年一月至民國七十六年十二月,總共有十二例胼胝體形成不良做過電腦斷層攝影檢查,我們將其診斷要點做了回顧及評估,提供放射醫學界的同仁們參考。
Dysgenesis of the corpus callosum is one of the most common congenital malformations of the brain recognized on CT. The characteristic features(superscript 3,11,17) of uncomplicated corpus callosum dysgenesis in CT include: a) widely separated, parallel or nonconverging lateral ventricles; b) ”batwing” or ”Bullhorn” appearance of the frontal horns; c) disproportionate enlargement of the occipital horns; d) enlargement of the interventricular foramen; e) high riding third ventricle which may be enlarged and have a tear-drop or rhomboid appearance; f) the interhemispheric fissure sign. In a retrospective study of twelve cases, the recognized CT manifestations of this disorder are reviewed and assessed.