Pulmonary Alveolar Proteinosis: Report of Four Cases

肺泡蛋白質沉積症：4例案例報告

林倩薏(Chien-Yi Lin) ； 許清寅(Chin-Yin Sheu) ； 陳培然(Pei-Jan Chen)

《中華放射線醫學雜誌》 24卷6期 (1999/12) Pp. 243-247

摘要

肺泡蛋白質沉積症是一種少見的肺部疾病。本文討論四位患者的臨床症狀及影像發現：其中三例為原發性，一例為續發性。本症臨床症狀多為長時間且不具診斷性，典型影像發現則為肺泡浸潤且時間不同浸潤區域會有所改變，常會誤診為肺炎。最常用之治療方法是氣管肺泡灌沖法。本病於有典型影像發現之患者但症狀長期且輕微與影像無法配合者應優先考慮。

關鍵字

蛋白質沉積症 ； 肺，浸潤 ； 肺，灌洗

並列摘要

Pulmonary alveolar proteinosis (PAP) is an uncommon disease of the lung. Clinical manifestations and imaging findings of 4 cases of PAP are reviewed: 3 primary and 1 secondary. Clinical symptoms are usually nonspecific and long term. Characteristic imaging findings are of an alveolar consolidation process involving different areas at different times. The condition is commonly misdiagnosed as pneumonia. Bronchoalveolar lavage is the best treatment up to now. PAP should be considered first in patients with characteristic imaging findings whose clinical symptoms are usually long term and nonspecific and too mild when correlated with imaging findings.

並列關鍵字

Proteinosis ； Lung, consolidation ； Lung, lavage