脂肪性心房中隔肥大症並非真正的腫瘤,它相當罕見,通常於超音波檢查時偶然發現,主要的臨床表現為心率不整、可導致病人猝死。我們在此提出一個合併脂肪性心房中隔肥大症與肥大性心肌病變的病例,其初始之胸部超音波檢查發現為心肌肥大症及高迴音之心房腫瘤。經磁振造影掃描發現其心房中隔上有脂肪侵潤,顯示其為脂肪性心房中隔肥大症合併肥大性心肌病變。依我們所知,脂肪性心房中隔肥大症與肥大性心肌病變之合併發生被假設為偶發性且尚未有文獻報告。當脂肪性心房中隔肥大症之特徵在超音波檢查為模擬兩可時,磁振造影掃描可作為重要之輔助診斷工具。
Lipomatous hypertrophy of interatrial septum, usually found in echocardiography, is a rare non-neoplastic disease entity, which may cause arrhythmia or sudden death. We reported a case of LHIS associated with hypertrophic cardiomyopathy, which was suspected a hyperechoic intraa-trial tumor in transthoracic echocardiography. Magnetic resonance imaging showed fat infil-tration of the interatrial septum, indicating lipoma-tous hypertrophy in addition to hypertrophic myocardium. Combined HCM and LHIS were assumed incidental but had not been reported to our knowledge. Characteristic MR imaging of LHIS is an important supplement to echocardiography with ambiguous findings.