腹骨盆腔脂肪瘤瀰漫性增生(abdominopelvic lipomatosis)是一種極罕見的良性腫瘤,臨床上經常誤認為惡性腫瘤。我們報告一位八歲小女孩因急性下腹疼痛至本院就診,身體檢查發現下腹有明顯腫瘤合併壓痛症狀,經超音波與電腦斷層檢查顯示有一巨大腫瘤位於腹骨盆腔內。手術切除時發現腫瘤內有壞死脂肪細胞,經送病理冰凍切片檢查,病理報告顯示為一腹骨盆腔良性脂肪瘤瀰漫性增生合併壞死病灶。
Abdominopelvic lipomatosis is a rare benign disease. Few cases have been reported in the literature, Most cases were characterized by an abnormal overgrowth of adipose tissue mainly in the abdominopelvic space. We reported here an 8-year-old girl with torsion of pelvic lipomatosis causing severe acute abdomen. The fat necrosis mimicking liposacroma was been noted during surgical excision. Frozen section of histopathology revealed torsion of lipomatosis. It is important to make a differential diagnosis of a pelvic neoplasm, mimicking malignancy. The best choice of treatment is surgical removal of the pelvic mass, and pathological examination.