鐮狀網膜皺壁

A Case Report of Falciform Retinal Folds

蔡瓊瑶(Chawn-Yow Tsai) ； 郭芳洲(Fang-Chow Kuo) ； 黃榮輝(Rong-Fui Huang)

《中華民國眼科醫學會會刊》 19卷 (1980/05) Pp. 165-171

https://doi.org/10.30048/ACTASOS.198005.0025

摘要

鐮狀網膜皺壁(falciform retinal folds)是一種罕見的先天性異常，它被認為是屬於殘遺增生性初次玻璃體（persistent hyperplastic primary vitreous簡稱PHPV）的後型。在眼底鏡下可見一黃白色隆起的皺壁由網膜伸入玻璃體，它的走向通常由視神經盤到周邊網膜，而它的位置大多在網膜的下顯象限，常合併黃斑部移位；病人視力通常不好，且伴有小角膜畸型、斜視及眼球震顫等異常。本文報告一鐮狀網膜皺壁病例，並對其病因、遺傳性、組織病理學、鑑別診斷及治療方法等加以討論。

並列摘要

This paper is to report a 21-year old male patient who was diagnosed as falciform retinal folds on his right eye with poor visual acuity, strabismus and macular displacement.
His mental condition was normal and the systemic examination included skull x-ray, chest x-ray and laberatory findings were within normal limit. Birth history revealed that he was born at term with normal birth weight and no history of perinatal oxygen therapy.
The local examination included visual acuity, tonometry, slit lamp examination, visual field, fundus, and fluoresceia angiography were discussed in this paper.
The etiology, histopathology, hereditability, differential diagnosis and management of the congenital anomaly were discussed in this paper too.

並列關鍵字

Falciform retinal folds ； PHPV persistent hyperplastic primary vitreous ； Imperfect differentiation ； Retinal rosettes