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柯滋氏型色素性視網膜變性以冷凍及雷射光凝治療之一病例報告
Coats'-Type Retinitis Pigmentosa Treated with Cryotherapy and Laser Photocoagulation-Case Report
摘要
本文報告一名十四歲男性病患，有十年的夜盲症病史及家族史，其眼底檢查除可見色素性視網膜變性的變化外，兩眼均有視網膜血管曲張、微細血管瘤、視網膜下脂質滲出和沈積，及滲出性視網膜剝離。左眼並發現有無脂質滲出的早期血管變化。經過一年半的治療追踪過程中，左眼經過局部雷射光凝治療後脂質浮出有減退現象，但視網膜變性及玻璃體纖維化仍持續進行；右眼發現時眼底已呈嚴重的晚期病變，雖經過冷凍及雷射治療，仍未能避免全盲的命運。在眾多的色素性視網膜變性的病人中，早期發現此種特殊病變然後給予治療。以避免黃斑部功能早期受損，是臨床醫師應特別留意的。
關鍵字
無資料並列摘要
A 14 years old boy (average)c 10 years history of tetinitis pigmentosa was found to have Coats'-like vasculopathy in both fundi, including telangiectatic & aneurysmal retinovascular changes with lipid exudation, neovascularization, exudative & tractional retinal detachment. Early pre-exudative vasculopathy, which was infrequently documented, was also found in some area of left fundus. In the more severely affected right eye, there were chronic retinal detachment & heavy lipid deposit involving macula and cryotherapy failed to restore vision. Extensive laser photo-coagulation in left eye seemed to arrest the exudation process although the vitreous traction & retinal degeneration still progressed. The detection & treatment of this rare vascular complication of retinitis pigmentosa remained a challenge to clinician.