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殘遺增殖性原發性玻璃體症(PHPV)伴有深度近視、弱視與斜視之病例報告
Persistent Hyperplastic Primary Vitreous (PHPV) with High Myopia, Amblyopia, and Strabismus-6 Cases Report
摘要
殘遺增殖性原發性玻璃體症(PHPV)屬於一種少見的胚胎眼球發育異常，依照眼球異常的部位不同分成前、後型，後型患者常合併視網膜和視神經的異常，因此後型的視力通常很差。本文報告六例殘遺增殖性原發性玻璃體症(PHPV)病例，皆為單側性疾患，其中3位為後型，另外3位是合併前後型患者，6名患者都沒有接受手術治療，患眼視力除了一位達到0.15，其餘都不到0.01，高度近視4位，眼球震顫(nystagmus)兩位，光天性白內障也有兩位，其餘外眼或身體的異常有先天性眼皮下垂(congenitall ptosis)、眼瞼血管瘤(hemangioma)、異位性肋骨(extra rib)。文中並回顧國內外之文獻報告，對此症的命名、分類、臨床特徵、診斷、治療、預後加以敘述。
關鍵字
無資料並列摘要
Persistent hyperplastic primary vitreous (PHPV) is a rare congenital anomaly and is described clinically as anterior or posterior type. Poor visual outcome was noted in the posterior PHPV. We presented 6 cases of persistent hyperplastic primary vitreous(PHPV) which are all unilateral eye involvement. All were pure posterior type or combined antero-posterior type of PHPV. Only 1 patients had better visual acuity (0.15). Another 5 patients had poor visual acuity (＜0.01). 4 cases had myopia. Nystagmus, congenital cataract, congenital ptosis, hemangioma, and extra rib were also noted in our cases report. At last we reviewed articles to discuss nomenclature, classification, clinical features, diagnosis, treatment, and prognosis of PHPV.