- 期刊
Congenital Pulmonary Venolobar Syndrome in Adults-Two Case Reports
先天性肺靜脈葉症候群－兩個病例報告
摘要
先天性肺靜脈葉症候群(congenital pulmonary venolobar syndrome, CPVS)是一種罕見的胸腔先天性的異常，可能單獨出現或合併其他異常疾病。先天性肺靜脈葉症候群中常見的要素包括肺部發育不全、部分肺靜脈回流異常、肺動脈缺乏、月市隔離、肺部的系統性動脈化、下腔大靜脈缺乏及副橫膈膜的發生；少數的要素包含氣管三分支化、橫膈膜膨出、部分橫膈膜缺乏、馬蹄形肺臟、食道和胃部的隔離肺、上腔大靜脈異常及左心包月莫的缺乏。在此我們提出兩個先天性肺靜脈葉症候群的病例，一個是典型的scimitar症候群，表現出右側肺動脈灌流至下腔大靜脈；而另一位病例則是左側部分肺動脈灌流至左側臂頭靜脈。在此並回顧歷年來與此種病例相關的文獻報告。
並列摘要
The congenital pulmonary venolobar syndrome (CPVS) is a rare congenital abnormality of the thorax that may appear singly or in combination. The common components of CPVS include hypogenetic lung, partial anomalous pulmonary venous return, absence of a pulmonary artery, pulmonary sequestration, systemic arterialization of the lung, absence of the inferior vena cava, and an accessory diaphragm. The rare components of CPVS include tracheal trifurcation, eventration of the diaphragm, partial absence of the diaphragm, horseshoe lung, esophageal and gastric lung, anomalous superior vena cava, and absence of the left pericardium. Herein, we present 2 young adult patients with CPVS. The first had a case of classic scimitar syndrome with right pulmonary venous drainage into the inferior vena cava. The other presented with partial anomalous drainage of the left pulmonary vein into the left branchiocephalic vein. A literature review is also included.