- 期刊
Tracheobronchomegaly Presenting as Tracheomalacia: A Case Report
氣管支氣管巨大症表現為氣管軟骨軟化：病例報告
摘要
氣管支氣管巨大症（tracheobronchomegaly，又稱Mounier-Kuhn syndrome）是一個以氣管及支氣管擴大為特徵的罕見先天性疾病。臨床表現通常於30至50歲左右以反覆肺部感染、氣管憩室或支氣管擴張症來表現。診斷主要是靠影像學，包括胸部X光、支氣管鏡或胸部電腦斷層。儘管全世界至今只有大約100個病例被呈現，但實際的發生率仍然不知道。治療上主要包含呼吸道清潔、抗生素、支架置放術，甚至極少數接受肺臟移植。此文中我們呈現一個腦傷後接受氣管內插管的病人出現早發性氣囊漏氣之現象；首先懷疑氣管軟骨軟化（tracheomalacia），但經過進一步檢查我們確認一個氣管內管氣囊漏氣的罕見原因為氣管支氣管巨大症。（胸腔醫學2011；26：332－337）
並列摘要
Tracheobronchomegaly, also called Mounier-Kuhn syndrome, is a rare congenital condition characterized by a dilated trachea and main bronchi. It often presents recurrent pulmonary infections, tracheal diverticulosis, or bronchiectasis in the 3rd or 4th decade of life. Diagnosis is made by chest X-ray, bronchoscopy or chest computed tomography scan. Although approximately 100 cases have been reported, the true incidence remains unknown. Treatment includes airway hygiene, antibiotics, stent placement, and rarely, lung transplantation. Herein, we report the case of a patient with an early onset of air leakage through the peri-cuff space after intubation for head injury. He was treated as having tracheomalacia at first. Finally, tracheobronchomegaly, a rare cause of endotracheal tube air leakage, was confirmed after comprehensive study. (Thorac Med 2011; 26: 332-337)