- 期刊
Malignant Eccrine Poroma of the Scalp-One Case Report
惡性汗管瘤的臨床經驗－病例報告
摘要
惡性汗管瘤是相當少見的表皮汗管腫瘤，在1963年首次由Pinkus及Mehregan提出，過去約有100個病例在文獻中提出，依過去記錄，多發生於老年人及下肢特別是足部，可以單一結節或息肉狀腫塊等多種臨床表現，並且可以臟器，淋巴或表皮轉移。我們報告一例79歲男性頭皮惡性汗管瘤的病人，其腫瘤以一再的頭皮腫瘤復發及頸部皮膚轉移來表現。我們採用廣泛圍的手術切除來治療病患，每次手術切除後的重建也相當成功，術後並未接受附加化學或放射治療，病人於病發後三年死因腫瘤顱內轉移合併中樞神經系統感染而病故，我報告這個病例並回顧相關文獻。
關鍵字
無資料並列摘要
Malignant eccrine poroma is a rare cutaneous neoplasm of sweat ductal origin. The term was first introduced by Pinkus and Mehregan in 1963 to describe epidermotropic eccrine poroma. About 100 cases have been reported in medical literature. It usually happens in the old age. It can be a single nodule, polypoid or ulcerative tumor. Distant visceral, regional lymphatic and cutaneous metastases have been reported in previous literature. A case of 79-year-old male with repeated recurrent scalp malignant eccrine poroma and neck skin metastasis is presented. Wide excision with free surgical margin was our strategy. The defects after tumor excision were reconstructed successfully in each operation. No adjuvant radiotherapy or chemotherapy was done due to unpredictable results. No visceral or lymph node metastasis were noted during this period. The patient died of multiple organ failure due to infection of central nervous system 3 years after disease occurrence. We discuss this case and review the past reports.