Ameloblastoma is a benign neoplasm of epitelial odontogenic origin, slowly growing, locally invasive and it is the most common odontogenic tumor in the Jaws. The purpose of the present study was to report a ameloblastoma case which is rare location, emphasing the clinic, operation and histopathological aspects that are relevant for the diagnosis and treatment of this pathology. This case was seen in a male child who was seven years old. Some diagnostic methods such as introoral and external examinations, radiographic and CT imaging systems were used to diagnose this case. The lesion in the case was removed totally with inside and outside maxiller sinus. It was determined a mass which is exopyhitic and sesil implantation and was measured as 2.5 cm. No complication was observed during and after surgery. This case was diagnosed as ameloblastoma after histopathological examination. The patient was monitored during 48 months after surgery and no signs were observed in relation to recurrence during monitoring.