一名三歲小女孩出生後由健檢發現罹患先天性心臟疾病,包含心房中膈缺損(atrial septal defect, ASD)、肺動脈瓣狹窄(pulmonary valve stenosis, PVS)及三心房症(cor triatriatum sinistrum, CTS),除心雜音外無任何呼吸困難、倦怠、發紺等症狀,臨床建議以心臟超音波持續追蹤心房中膈缺損及三心房症變化情形。日前因左上胸骨緣收縮心雜音,安排心導管檢查,發現左側肺靜脈血液上行經膨大的無名靜脈匯入上腔靜脈;為確認左側肺靜脈連接狀況,另以電腦斷層血管攝影檢查(computed tomography angiogram, CTA)作鑑別診斷。電腦斷層影像上可見左心房內分隔成兩腔室證實三心房症,並運用後處理volume rendering技術,影像呈現左肺靜脈為心上型部分肺靜脈回流異常(partial anomalous pulmonary venous return, PAPVR)。
Patient is a three years old girl who suffered from congenital heart disease combined atrial septal defect (ASD), pulmonary valve stenosis (PVS) and cor triatriatum sinistrum (CTS). These findings were diagnosed by health examination. She has no breathlessness, fatigue, or cyanosis but heart murmur was noted and suggested regular follow up. The pediatrician is used to check cardiac sonography the change of ASD and CTS via cardiac sonography. Diagnostic cardiac catheterization was performed recently due to the systolic murmur at left upper sternal border, catheterization result showed that left pulmonary venous blood flow goes upward through enlarged left innominate vein into superior vena cava (SVC). According above findings, computed tomography angiogram (CTA) is performed in order to check left pulmonary venous connecting pathway. CT images showed left atrium was separated from a membrane into two chambers, and supracardiac type of left pulmonary vein partial anomalous pulmonary venous return(PAPVR)present by volume rending post-process.