Acute hemorrhagic presentation of spinal schwannoma is an event rarely seen. We had ever reported a 63-year-old male presenting with acute spinal cord compression caused by a long segment of intradural extramedullary schwannoma with hemorrhage and atypical enhancement pattern. The magnetic resonance image findings included a long segmental irregular contour, intermediate signal intensity on T1-weighted images, heterogeneous and foci of low signal intensity on T2-weighled images and segmental enhancement of the lesion, all of which is highly atypical for schwannoma. Emergency surgical decompression was performed and the pathologic results have proved the existence of spinal schwannoma.