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類澱粉沉積心肌病變的治療現況

摘要


類澱粉沉積心肌病變是一種罕見心臟疾病,隨著現代核子醫學造影檢查的進步,部分類澱粉沉積心肌病變已不需透過侵入性的心肌切片來診斷。而過去針對類澱粉沉積心肌病變之治療方法有限,大都採支持性療法或肝臟移植,但隨著醫學的進步,針對不同分類的類澱粉沉積心肌病變正積極研發適切的藥物治療,新興藥物tafamidis已經獲得核准使用於轉甲狀腺素蛋白類澱粉沉積心肌病變(transthyretin amyloid cardiomyopathy, ATTR-CM)的病患上。診斷與治療的進步促使類澱粉沉積心肌病變逐漸獲得關注,本篇著重在介紹類澱粉沉積心肌病變的治療。

參考文獻


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