Oropharyngeal hairy polyp is a rare developmental malformation. Derived from the ectoderm and mesoderm, this benign tumor has generally been classified as dermoid, teratomatous, or hamartomatous in the past. Most originate either as pedunculated or sessile masses in the oro-nasopharyngeal region and usually presents with signs of upper aerodigestive tract obstruction. A full-term newborn girl was evaluated for a protruding oral mass and noisy breathing at birth. There was a soft, 5×2×1 cm, skin-covered, pedunculated mass that arose from the lateral aspect of the uvula and protruded from the oral cavity. The mass was removed without complication using CO2 laser excision and tissue histology was consistent with that of a hairy polyp. Subsequent follow-up showed satisfactory healing and no local recurrence. Oropharyngeal hairy polyps are rare with the life-threatening potential to cause airway obstruction. A review of the literature is discussed.