摘要
先天性鼻部中線皮樣囊腫和瘻管是罕見的先天性異常。這些異常可存在於鼻腔內，但大部份存在於外鼻部；除了上述部位，偶而也可以在鼻竇、眼眶、顱腔及腦硬膜中樞神經等處發現。至於外鼻部的異常，則在出生或兒童時期，可以看到鼻樑中央有凹點的腫塊。最好的診斷工具是加入顯影劑的電腦斷層攝影或核磁共振攝影。治療方法是以顯微手術切除該病灶並注意該病灶是否與中樞神經相連，若相連則需照會腦神經外科。 本文提出一名患有鼻部皮樣囊腫的8歲女孩病例，她的病灶位於鼻樑中央並經鼻骨侵入到鼻中隔上蓋骨，但未侵入腦硬膜。文中針對鼻部皮樣囊腫的診斷、治療、胚胎形成與病理變化提出討論。
關鍵字
無資料並列摘要
Midline congenital nasal dermoid cysts and sinuses are rare congenital anomalies with occasional central nervous system connections. Although some of the cases may present intranasally, most of them exhibit as external nasal masses with a tiny dimple along the midline of the nasal bridge visible at birth or in early childhood. Other extranasal presentations may be located in the paranasal sinuses, orbit, dura, skull ect. The most useful diagnostic study is CT or MRI with radiopaque contrast medium injected into the sinus tract. Microsurgical excision of the dermoid cysts, sinus tracts, and presumptive CNS connection is the treatment of choice. The following case report of a nasal dermoid cyst is presented along with a discussion of its deagnosis and management.