Neuroendocrine neoplasms of the larynx are a rare group of tumors that are thought to be arised from amine precursor uptake and decarboxylase (APUD) cells or the dispersed neuroendocrine cell system. Suggested embryonic sites of origin include the neural crest, ectoderm, and endoderm. The recent World Health Organization (WHO) classification scheme divides these tumors into three groups: carcinoid tumor, atypical carcinoid tumor, and small cell carcinoma. In October 1994, we encountered a 74 year old man who had suffered from dysphagia for several months. A larynogoscopic biopsy on a whitish irregular lesion at the right arytenoids was perfomed. The pathologic report was an atypical tumor. Computed tomography of the neck showed no evidence of regional metastasis. The tumor was removed by laser laryngomicrosurgery. He has been regularly followed for 22 months. No evidence of recurrence was noted.