界限性淋巴管瘤－兩病例報告

Lymphangioma Circumscriptum Report of Two Cases

董光義(Kwang-Yi Tung) ； 歐聖運(Shuan-Yuan Ou) ； 黃文成(Wen-Cheng Huang) ； 劉國威(Kwok-Wai Lau)

《中華民國重建整形外科醫學會雜誌》 3卷3期 (1994/09) Pp. 170-175

https://doi.org/10.7096/JPRSA.199409.0170

摘要

界限性淋巴管瘤是一個罕見的疾病，臨床上的特徵是皮膚上一個界定的區域內出現成羣的小水泡或小血泡。本文報告兩個處理困難的病例並作文獻回顧。組織病理學檢查可見由皮膚的乳突層至皮下組織中有許多非常擴大但仍只具有單層扁平內皮細胞的淋巴管。真正的致病原因仍不明，但形成表層小水泡的真正病因可能是深層皮下組織中的大型淋巴管池槽。MRI可以幫助診斷此疾病真正的範圍與深度。對於範圍較大的病灶可採用廣泛性的皮下病灶組織切除加上適度的皮膚切除來治療，而二氣化碳雷射汽化治療是一種理想的症狀舒減療法。

並列摘要

Lymphangioma circumscriptum is a rare disease, which is characterized clinically by grouped thin-walled translucent or blood-tinged vesicles on a circumscribed area of the skin. Our experience with 2 difficult cases and a literature review were presented. The histopathological figures are grouped cystic spaces lined by flattened endothelial cells, located in the papillary layer of the dermis continuing down into the subcutaneous fat. The etiology is unclear; but it has been postulated that the deeper component of large lymphatic cisterns gave rise to the superficial vesicles. MRI may be used to estimate the extension and depth of involvement of this disease. Wide subcutaneous excision plus adequate skin excision could be the treatment for extensive lesions; and carbon dioxide laser vaporization might be a palliative symptomatic treatment for superficial components of this cutaneous lymphangiomas.