十二指腸旁疝氣為見之先天性疾病,其發之原因仍是中腸(midgut)旋轉錯誤所致。它約佔所有內部疝氣之53%。我們提出一例以急性腹痛為表徵之病例報告,並覆閱有關文獻。致謝:本文繪圖承蒙袁珠山大夫協助,特此誌謝。 一37歲女性病患,懷孕5個多月時,於右鼻腔出現一紅色腫瘤,造成鼻塞及鼻臱衂。分娩後腫瘤仍繼續存在。組織病理顯示腫瘤主要由許多大小不一的管腔及紡綞形間質細胞所構成。免疫組織化學檢查,在腫瘤管腔內襯細胞及紡綞形間質細胞,除Factor VIII及UEAI呈陽性反應外,尚具有動情淚素柔黃體淚素接受器。吾人提出此病例,並討論其病因及荷爾蒙接受器。
A 37 year old female patient had a red tumor in her right nasal cavity since she was more 5 months pregnant. The tumor caused nasal obstruction and epistaxis, and still existed after delivery. Histopathologic examination showed numerous irregular clefts and spaces scattered through the specimen, the intervening stroma had varied cellurality with aggregates of spindle-shaped cells of uniform character. In immunohistochemical studies, besides Factor VIII and UEAI reaction were postive, we also found the presence of edtrogen and progesterone receptors in vascular lining cells and stroma spindleshaped cells. A discussion of etiology and hormone receptor is included.