- 期刊
Bilateral Laparoscopic Gonadectomy for Testicular Feminization Syndrome
經腹腔鏡兩側睪丸切除治療睪丸女性化症候群
摘要
雄性激素接受器基因缺損會造成睪丸女性化症候群，並影響睪丸的下降，為避免兩側腹腔內睪丸產生惡性化的危險，青春期時需施行手術將睪丸切除及服用雌性素維持正常女性性徵的發育。本報告敘述一位二十二歲主訴原發性無月經的女性經超音波檢查無子宮的存在，實驗室數據並顯示為男性 46 , XY 染色體及血中濾泡刺激激素上昇，電腦斷層檢查可定位兩側未下降睪丸的位置。施行腹腔鏡手術切除兩側睪丸較傳統剖腹探查手術優在於可縮短住院及恢復的時間。
關鍵字
無資料並列摘要
Defects of androgen receptor gene lead to testicular feminization syndrome, which is one of the most common etiology of male pseudohermaphroditlsm. A 22-year- old phenotypic female with primary amenorrhea and insomnia is presented. Gross appearance revealed sparse axillary and pubic hair, poor breast development, clitoromegaly and absence of vagina. Ultrasound demonstrated no evidence of the uterus or adnexal structures, but the prostate gland was found. The laboratory data showed elevated follicle-stimulating hormone and a male 46, XY karyotpe. Computed tomography localized the position of bilateral undescending testes, which were removed by operative laparoscopy procedures later. The patient was discharged without complication postoperatively.
延伸閱讀
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