Chronic thromboembolic pulmonary hypertension, a disease frequently misdiagnosed

Margita Belicová ； Veronika Jankovičová ； Marian Mokáň

《International Journal of Case Reports and Images (IJCRI)》 8卷1期 (2017/01) Pp. a11+51-56

https://doi.org/10.5348/ijcri-201706-CR-10745

摘要

Introduction: Chronic thromboembolic pulmonary hypertension results from incomplete resolution of a pulmonary embolus, leading to pulmonary hypertension and progressive right heart failure and death. Contemporary pharmacological and especially surgical treatment possibilities offer hope for the patient's full recovery, but an early diagnosis is crucial for success. Case Report: A 56-yearold white female, who despite thrombolytic therapy and next appropriate anticoagulation, was re-hospitalized six years after acute pulmonary embolism for severe pulmonary hypertension, due to chronic thromboembolic pulmonary hypertension. Before the diagnosis was established, she underwent lungs biopsy because of suspected interstitial lung disease and a bone marrow aspirate and biopsy because of progressive polycythemia. After chronic thromboembolic pulmonary hypertension was established, she underwent successful pulmonary endarterectomy. Conclusion: Chronic thromboembolic pulmonary hypertension is frequently misdiagnosed in clinical practice. This report aims to increase the awareness of clinicians towards an accurate diagnosis of the disease, which is necessary for the early referral of chronic thromboembolic pulmonary hypertension patients for operability, pulmonary endarterectomy.

關鍵字

Chronic thromboembolic pulmonary hypertension ； Pulmonary embolism ； Pulmonary endarterectomy ； Pulmonary hypertension