透過您的圖書館登入
IP:3.145.175.7

摘要


P-J症候群是一種罕見的疾病,在國內只有零星的病例報告。我們收集過去十年來在三軍總醫院診斷為P-J症候群的十個病例並加以臨床分析。這十例病患均具有P-J症候群的特點-皮膚黏膜色素沈著及腸胃道過誤瘤。這些過誤瘤可存在於腸胃道的任何部位,但以小腸為最常見。有五例因併發腸道套疊、出血及阻塞而接受手術治療。在切除的三十七個過誤瘤中有兩個黏膜上皮有發育不良現象。有一例併發兩側乳癌,另一例因腸道併發症,而於四年內接受了三次的剖腹手術。

並列摘要


The Peutz-Jeghers (P-J) syndrome is a rare condition and only few cases have been reported in Taiwan. We analyze the clinical data of 10 cases of P-J syndrome collected from 1985 to 1994 in Tri Service General Hospital (TSGH). Mucocutaneous pigmentation and gastrointestinal (GI) hamartomatous polyps, the characteric findings of P-J syndrome were presented in all these ten cases. The polyps in these patients with P-J syndrome were usually multiple and were found throughout the GI tract, mainly in the small intestine. Five cases received surgical intervention because of complications including GI intussusception, bleeding and obstruction. Two of total 37 resected hamartomatous polyps displayed mucosal dysplastic change. Another case developed bilateral infiltrating duct carcinoma of breast. One case reveived three times exploratory laparotomies for P-J syndrome related GI complications in four years.

延伸閱讀


  • Hsu, C. H., Yang, Y. H., Tasi, C. H., Wu, H. S., Hung, M. C., Wu, Y. J., Chou, D. A., Yang, J. C., & Huang, M. H. (2007). Peutz-Jeghers症候群引起腸套疊個案報告. 秀傳醫學雜誌, 7(3), 111-114. https://www.airitilibrary.com/Article/Detail?DocID=15610497-200710-7-3-111-114-a
  • Yang, M. T., Yang, C. C., Chu, L. W., Lee, W. T., Young, C., & Wang, P. J. (2002). Schwartz-Jampel症候群:一病例報告. Acta Paediatrica Taiwanica, 43(4), 220-223. https://doi.org/10.7097/APT.200208.0220
  • Chiang, H. J., & Wong, L. Y. (1978). Peutz-Jeghers氏症候羣. 中華放射線醫學雜誌, 3(3), 219-224. https://www.airitilibrary.com/Article/Detail?DocID=10188940-197809-3-3-219-224-a
  • 林棋民、蔡鶴峰、吳志順、馬鴻均(1995)。Peutz-Jeghers症候群:病例報告Journal of Medical Sciences16(3),182-188。https://www.airitilibrary.com/Article/Detail?DocID=10114564-199512-201306200025-201306200025-182-188
  • Tan, C. K., Tsai, F. J., Lin, C. C., Wu, J. Y., Yu, M. T., Hsu, S. L., Shi, Y. R., Chang, J. C. Y., & Lai, S. W. (2000). Wolf-Hirschhorn症候群:一病例報告. Acta Paediatrica Taiwanica, 41(1), 39-42. https://doi.org/10.7097/APT.200002.0039