摘要
發生在肝的血管脂肪肌瘤是一種少見的良性疾病，在西方及亞洲國家都發表過關於其臨床症狀、影像及病理表現的文獻。我們提出一肝血管脂肪肌瘤的病例報告，並藉此作一文獻回顧，此病例是一診斷爲肝的血管脂肪肌瘤的六十歲女性，她最初的表現是食慾降低、偶發性嘔吐及上腹痛。腹部電腦斷層發現左上腹有一個巨大的腫瘤，由肝動脈的分支供給其血流。內視鏡超音波及上消化道攝影均認爲此腫瘤於胃外造成壓迫。病思後來接受手術，術中發現腫瘤是由肝的左葉長出，於是做了部份左側葉切除術，該腫瘤大小爲20×15×12.5公分，重1,947克，顯微鏡下可見其成份是脂肪細胞、血管及平滑肌的混合。多數的紡錘狀及表皮狀細胞呈現陽性的SMA染色，而對HMB-45抗體的結合呈陽性反應，這些現象符合血管脂肪肌瘤的診斷。
並列摘要
Angiomyolipoma is a relatively rare benign tumor in the liver Literatures about the clinical presentations, image and pathological findings have been published in Western and Asian countries. Here we presented a case of hepatic angiomyolipoma and summarized the literature review of this disease. A 60 year-old woman complained of post-prandial fullness and loss of appetite for more than two weeks. Abdominal CT showed a huge mass, supplied by the branch of hepatic artery, over left upper quadrant. Endoscopic ultrasound and upper gastrointestinal series revealed the stomach was compressed by an external mass. She was operated and the tumor was in the left hepatic lobe. Left lateral segmentectomy was performed and the tumor was measured 20 x 15 x 12.5 cm in size and 1,947 g in weight. Microscopically, it was composed of mixtures of adipose tissues, vessels and smooth muscle cells. Most of the spindle cells and the epitheloid cells were immunoreactive to smooth muscle actin and HMB-45 antibody. Those findings were compatible with angiomyolipoma.
延伸閱讀
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