MR Images of Moyamoya Disease: Report of a Case

毛毛樣腦血管症在磁共振造影的表現：一病例報告

陳明聰(Ming-Chang Chen) ； 黃國茂(Kou-Mou Huang) ； 廖漢文(Hon-Man Liu)

《慈濟醫學雜誌》 6卷4期 (1994/12) Pp. 281-285

https://doi.org/10.6440/TZUCMJ.199412.0281

摘要

毛毛樣腦血管症是一罕見之疾病，但在年經中風的病人本疾病必須列入診斷之一。我們報告的病例，為一五歲小女孩，曾經有多次中風的病史，住院做過電斷層，磁共振造影及腦血管攝影檢查。典型毛毛樣腦血管症為內頸動脈，前和中腦動脈產生進行性狹窄並發生很多側枝循環來供應腦部營養。磁共振造影比電腦斷層優越處因前者不必施予顯影劑即能顯現異常血管，包括內頸動脈，前和中腦動脈狹窄及腦實質內側枝血管等的。磁共振造影亦有較佳的組織對比，因此對腦實質的病變有較好的偵測能力。而腦血管檢查為侵略性攝影，因此當臨床懷疑毛毛樣腦血管症時，磁共振造影或許可做為第一線檢查工具。(慈濟醫學1994; 6: 281-285)

關鍵字

moyamoya disease ； MRI

並列摘要

Moyamoya disease is a rare disease entity, but it should be taken into consideration in young stroke patients. We report a five-year-old girl with repetitive hemiparesis who underwent CT, MRI and angiographic examinations. The characteristic features of moyamoya disease are progressive narrowing of the supraclinoid portion of the internal carotid artery and its main branches, followed by many collaterals. MR images without contrast medium enhancement can demonstrate these abnormal vessels well. They are diminished arteries of the circle of Willis and the development of parenchymal collaterals. MR also provides better tissue contrast to depict the parenchymal manifestations than that of CT study. Angiography is an invasive but diagnostic procedure. MRI study may be an alternative imaging modality to evaluate the cases with clinical suspicion of moyamoya disease, non-invasively. (Tzu Chi Med J 1994; 6: 281-285)

並列關鍵字

毛毛樣腦血管症 ； 磁共振造影