Clinical and Radiological Manifestation of Albright's Syndrome: Report of Albright's Syndrome: Report of 3 Cases

阿布萊德氏(Albright's)症候群的臨床及放射線檢查的表現：三個病例報告

周琪(Julie Chi Chow) ； 曾旭明(Yuk-Ming Tsang) ； 黃天祥(Tien-Shang Huang) ； 黃國茂(Kou-Mou Huang) ； 徐劍耀(Jane Chien-Yau Hsu)

《中華放射線醫學雜誌》 17卷2期 (1992/06) Pp. 159-164

摘要

從1980-1989年共有三例阿布萊德氏症候群，都具有以下三項特徵：多發性骨纖維性結構不良，皮膚之異常色素沈著及內分泌功能之異常。其中有兩例男性，一例女性，年齡由35至48歲。此三例都患有胸部及大股骨之多發性骨纖維性結構不良(polyostotic fibrous dysplasia)，併有皮膚色素沈著與一般文獻報告之Albright's syndrome之表現差不多。惟本文發現2例hypogonadism則與以往之報告不同，或可將hypogonadism列入整個內分泌異常之另一種表徵。

關鍵字

阿布萊德氏症候群 ； 骨結構不良

並列摘要

We report 3 cases of Albright's syndrome consisting of the triad of polyostotic fibrous dysplasia, cafe au lait spots and various endocrinal abnormalities, which were encountered in the period from 1980 to 1989. There were 2 males and 1 female, with age ranging from 35 to 48 y/o. All of them had polyostotic fibrous dysplasia mainly involving thoracic cage and femoral bone, pigmented skin spots, and endocrine disorder. Two had hypogonadism which was not commonly reported. It is our purpose to bring up the possibility of Albright's syndrome as a differential diagnosis when polyostotic fibrous dysplasia is seen.

並列關鍵字

Albright's syndrome ； bone, dysplasia