Primary Mediastinal Hemangiopericytoma: A Case Report

原發性縱膈腔血管外皮細胞瘤：病例報告

曾芸軒(Yun-Hsuan Tzeng) ； 藍功堯(Gong-Yau Lan) ； 鍾明燈(Ming-Teng Chung) ； 符振中(Jene-John Fu)

《中華放射線醫學雜誌》 26卷2期 (2001/04) Pp. 91-96

摘要

原發性縱膈腔血管外皮細胞瘤是非常罕見的腫瘤。我們提出一個病例並討論其臨床症狀、診斷、與放射學特徵。一位53歲女性病患主訴在求診前數個月開始出現咳嗽及呼吸困雖的情形。胸部X光攝影及電腦斷層掃描發現在她的左側縱膈腔有一界限清楚的腫塊，腫塊內並有壞死及鈣化。此病患接受了腫瘤切除術，最後的診斷為原發性縱膈腔血管外皮細胞瘤。就我們所知，僅有20例原發性縱膈腔血管外皮細胞瘤曾被報告於英文文獻中，且尚無一例發現鈣化的現象。我們在此提出首例觀察到中央鈣化的原發性縱膈腔血管外皮細胞瘤。

關鍵字

血管外皮細胞瘤 ； 縱膈腔 ； 鈣化 ； 電腦斷層攝影

並列摘要

Primary mediastinal hemangiopericytomas are very rare tumors. We present a patient with this disease and discuss the clinical symptoms, diagnosis, and the correlation of radiographic features. A 53-year-old woman complained of the cough and the dyspnea for months before consultation. The chest X-rays and computed tomography revealed a well-defined intensive enhanced mass in the left middle mediastinum with necrotic changes and calcification within it. The patient underwent left thoracotomy with tumor resection, and a final diagnosis of primary mediastinal hemangiopericytoma was made. To our knowledge, only 20 cases of primary mediastinal hemangiopericytoma have been reported in the English literature, but no patient was reported with calcification. We present the first case of a mediastinal hemangiopericytoma with central calcification.

並列關鍵字

Hemangiopericytoma ； Mediastunum ； Calcification ； Computed tomography (CT)