Mediastinal Lipoblastoma of Infancy:a case report

縱隔腔脂肪母細胞瘤：病例報告

李國泰(Kuo-Tai Li) ； 王超然(Chao-Ran Wang) ； 勞允澤(Wan-Chak Lo) ； 薛純(Chuen Hsueh) ； 池永昌(Wing-Cheong Chi)

《中華放射線醫學雜誌》 28卷6期 (2003/12) Pp. 397-401

摘要

縱隔腔脂肪母細胞瘤是一種罕見胚胎脂肪間質瘤，常發生在3歲之前，少於20例已發表在英文的文獻中。在所有小孩腫瘤中，脂肪母細胞瘤佔不到1%的發生率。四肢是它好發生的地方。我們報告此九月大女嬰孩有罕有病例，不同於過往例子，他們都是年紀較大時才被診斷。我們有電腦斷層攝影及磁振造影的影像討論。手術中，腫瘤完全被切除，並沒有併發症。組織報告中証實為包膜葉狀的脂肪母細胞瘤。

關鍵字

嬰孩 ； 脂肪母細胞瘤 ； 縱隔腔

並列摘要

Mediastinal lipoblastoma is a rare mesenchymal tumor of embryonal fat occurring predominantly in the first three years life. Less than 20 cases have been reported so far in the Western literature. Lipoblastomas constitute less than 1% of all pediatric tumors. The extremites are the most common location for this tumor. We presented a rare 9-month-old female infant case that differed from previously reported mediastinal lipoblastomas in those patients who were much older. The computed tomography (CT) and magnetic resonance image (MRI) features were discussed. At surgery, the tumor was removed without complication and histology demonstrated an encapsulated and multilobulated lipoblastoma.

並列關鍵字

Infancy ； Lipoblastoma ； Mediastinum