Langerhans Cell Histiocytosis with Lungs and One Rib Involvement: A Case Report

同時出現肺部和肋骨之藍格罕士氏細胞組織細胞症：病例報告

林建人(Chien-Jen Lin) ； 張晉民(Jinn-Ming Chang) ； 曾文盛(Wen-Sheng Tzeng) ； 馮瑤(Yao Fong) ； 蘇正川(Chang-Chuan Su)

《中華放射線醫學雜誌》 30卷1期 (2005/02) Pp. 35-39

摘要

肺部Langerhans cell histiocytosis(LCH)是一種稀有的疾病。典型的胸部CT影像特徵是許多奇形怪狀的囊狀空腔與一些細支氣管旁的小結，主要是分佈在上面三分之一的肺部。但是由於疾病進展關係，細支氣管旁的小結並非總是會表現出來。在組織學下證明是肺外LCH的病患中，如果high-resolution CT的特徵與肺部LCH一致的話就可以診斷是肺部LCH。最近我們遇到一位在組織學下證明是骨的LCH的病患。這位病患的肺部影像表現出許多奇形怪狀的囊狀空腔但卻沒有明顯的肺內的小結。

關鍵字

細胞組織細胞症 ； 肺，電腦斷層攝影 ； 肺部疾病 ； 肋骨，腫瘤

並列摘要

Pulmonary Langerhans cell histiocytosis (LCH) is a rare disease. The typical findings on chest computed tomography (CT) of this disease are multiple bizarre cystic spaces associated with small peribronchiolar nodules, predominantly in the upper third of both lungs. The peribronchiolar nodules are not always present due to the evolution sequence. For patients with histiologically proven extrapulmonary LCH, the diagnosis of pulmonary LCH is usually established if the findings on high-resolution CT are consistent with pulmonary LCH. Recently we encountered one patient with histiologically proven osseous LCH. The chest CT feature of this patient was multiple bizarre cystic spaces without obvious pulmonary parenchymal nodule.

並列關鍵字

Histiocytosis ； Lung, CT ； Lung, disease ； Rib, neoplasms