硬皮症合併全身紅斑性狼瘡與眼底疑似色素性視網膜炎的眼睛表現－病例報告

Ocular Findings of Suspected Retinitis Pigmentosa in Progressive Systemic Scleroderma Associated with Systemic Lupus Erythematosus-A Case Report

郭千能(Chein-Neng Kuo) ； 郭明倫(Min-Lun Kao) ； 郭錫恭(His-Kung Kou) ； 鄧美琴(Mei-Chung Teng)

《中華民國眼科醫學會雜誌》 40卷2期 (2001/06) Pp. 184-192

https://doi.org/10.30048/ACTASOS.200106.0016

摘要

Purpose: To report a case with unusual manifestations of atypical retinitis pigmentosa in ”Progressive systemic scleroderma” and ”Systemic lupus erythematosus”.
Methods: A case report.
Results: A 30-years-old woman with no significant family history was diagnosed ”Progressive systemic scleroderma” by biopsy improved for almost 14 years by dermatologists and ”Systemic lupus erythematosus” impressed for 6 years by rheumatologists. Constricted visual field, limited external ocular movement progressively and slightly exotropia (＜50 were noted for recent 2 years. Visual acuity was 0.6 in right eye and 0.5 in left eye. Fundus showed arteriolar attenuation, retinal bone-spicule with .fine dust-like pigments and hyperemic change of optic disc. Goldman visual field revealed Peripheral visual field defect and residual central island vision (ou). Fluorescein angiography showed delayed choroidal and retinal filling, retinal pigment epithelial window defect and leakage of dye from swelling optic disc.
Conclusion: The specific finding of this patient who is noted of suspected ”Retinitis pigmentosa” and ”Progressive systemic scleroderma associated with Systemic lupus erythematosus” concomitantly may be different from previous studies, so we present it.

並列摘要

Purpose: To report a case with unusual manifestations of atypical retinitis pigmentosa in ”Progressive systemic scleroderma” and ”Systemic lupus erythematosus”.
Methods: A case report.
Results: A 30-years-old woman with no significant family history was diagnosed ”Progressive systemic scleroderma” by biopsy improved for almost 14 years by dermatologists and ”Systemic lupus erythematosus” impressed for 6 years by rheumatologists. Constricted visual field, limited external ocular movement progressively and slightly exotropia (＜50 were noted for recent 2 years. Visual acuity was 0.6 in right eye and 0.5 in left eye. Fundus showed arteriolar attenuation, retinal bone-spicule with .fine dust-like pigments and hyperemic change of optic disc. Goldman visual field revealed Peripheral visual field defect and residual central island vision (ou). Fluorescein angiography showed delayed choroidal and retinal filling, retinal pigment epithelial window defect and leakage of dye from swelling optic disc.
Conclusion: The specific finding of this patient who is noted of suspected ”Retinitis pigmentosa” and ”Progressive systemic scleroderma associated with Systemic lupus erythematosus” concomitantly may be different from previous studies, so we present it.

並列關鍵字

Scleroderma ； Systemic lupus erythematous ； Retinitis pigmentosa ； Sclerolupus