The clinical manifestations of aortic dissection are highly variable. Although the majority of patients manifest typically with chest pain and radiation to the back or congestive cardiac failure, atypical presentations have also been documented that can be easily overlooked. We report a 47-year-old man who developed monocular blindness and visited our emergency department. Computed tomography of the chest at a later time revealed aortic dissection complicated by common carotid artery dissection. After successful surgical treatment, the patient was discharged uneventfully 29 days after admission. A high level of vigilance is required in order to diagnose carotid artery dissection when a patient presents with painless acute monocular visual loss.