Coronary artery fistula is a rare cause of acute myocardial infarction. We report a 58-year-old man who presented with acute chest pain. The electrocardiography showed slight ST-segment elevation in leads I, aVL, with ST-segment depression in leads II, III, aVF and V2-5. The biochemical markers of myocardial injury were elevated. Selective coronary angiography showed a coronary artery fistula originating from the distal left anterior descending artery to the left ventricle. Multidetector computed tomography confirmed this diagnosis and excluded the presence of other anomalies. He underwent successful transcatheter coil embolization and remained symptom free for 6 months.