Hughes-Stovin Syndrome in a Patient with Behçet's Disease-A Case Report

貝賽特氏病病人合併Hughes-Stovin症候群－病例報告

葉靖宇(Ching-Yu Yeh) ； 施崇鴻(Chung-Hung Shih) ； 王鋒杰(Fong-Chieh Wang)

《胸腔醫學》 21卷1期 (2006/02) Pp. 46-52

https://doi.org/10.29806/TM.200602.0007

摘要

Hughes-Stovin症候群為一非常罕見的疾病合併有多發性肺動脈瘤及深部靜脈栓塞或血栓靜脈炎。Hughes-Stovin症候群和貝賽特氏病是兩種已知會發生肺動脈瘤的非先天性、非感染性疾病。兩者之問的關聯性仍有爭議。我們報告一個非常罕見的病例為貝賽特氏病合併Hughes-Stovin症候群。病人一開始的表現為胸痛、咳血、發燒、寒顫及軀幹出現表面靜脈充血。胸腔核磁共振血管攝影、血管攝影、胸腔及腹部電腦斷層診斷出多發性肺動脈瘤及深部靜脈栓塞。反覆性口腔潰瘍、生殖器潰瘍及皮膚病灶診斷出貝賽特氏病。病人接受合併使用皮質類固醇、秋水仙素及環磷醯胺的治療。

關鍵字

Hughes-Stovin症候群 ； 貝賽特氏病 ； 肺動脈瘤

並列摘要

Hughes-Stovin syndrome (HSS) is a very rare disorder with a combination of multiple pulmonary artery aneurysms and deep venous thrombosis or thrombophlebitis. Hughes-Stovin syndrome and Behçet's disease (BD) are the 2 known non-congenital, noninfectious diseases that produce pulmonary aneurysms. The relationship between them is still controversial. We report a very rare case of Hughes-Stovin syndrome in a patient with Behçet's disease. The patient initially presented with chest pain, hemoptysis, fever, chills, and engorged superficial veins on the trunk. Multiple pulmonary artery aneurysms and deep venous thrombosis were ascertained by thoracic magnetic resonance angiography (MRA), angiography, and chest and abdominal computed tomography (CT). BD was diagnosed with recurrent oral ulcers, genital ulcers, and skin lesions. The patient was treated with combinations of corticosteroid, colchicine, and cyclophosphamide.

並列關鍵字

Hughes-Stovin syndrome ； Behçet's disease ； pulmonary artery aneurysms