- 期刊
Life-threatening Hemoptysis as Initial Presentation of Primary Sjögren's Syndrome: A Case Report
以危及生命之咳血爲初始表現的原發性修格蘭氏症候群－病例報告
摘要
在原發性修格蘭氏症候群的臨床表現中，肺部侵犯的頻率和型式有著很大的變異程度。一般而言，肺部侵犯通常都很輕微且進行相當緩和。然而，以支氣管擴張症合併大量咳血為初始表現者，目前並無報告案例。我們在此提出一位69歲女性，過去沒有肺部相關疾患和症狀，但因突發性大量咳血合併呼吸衰竭住院，後來才確診為原發性修格蘭氏症候群的個案。藉由此案例報告，我們希望能夠提醒臨床醫師，如果病患的胸部影像學顯示支氣管擴張症徵像，但臨床上並無典型症狀時，應該將會併發支氣管擴張症的全身性相關疾患列入鑑別診斷，包括原發性修格蘭氏症候群。
並列摘要
The reported frequency and forms of pulmonary involvement in patients with primary Sjögren's syndrome (pSS) vary widely, and pulmonary involvement in pSS is usually mild and slowly progressive. Bronchiectasis complicated with life-threatening hemoptysis as the initial presentation of pSS has not yet been reported. We report such a case in a 69-year-old woman. The findings of our case suggest that bronchiectasis caused by systemic diseases including pSS should be added to the list of differential diagnoses for life-threatening hemoptysis, particularly for those without the characteristic clinical features of bronchiectasis.
延伸閱讀
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