透過您的圖書館登入
IP:18.117.196.184
  • 期刊

Tracheobronchomegaly and Ankylosing Spondylitis: A Case Report and Literature Review

氣管支氣管巨大症與僵直性脊椎炎:病例報告及文獻回顧

摘要


氣管支氣管巨大症又被稱為Mounier-Kuhn症候群,是一種在氣管及支氣管會有顯著擴張且合併有慢性呼吸道感染的獨特疾病。其病因源於氣管及支氣管壁的彈性及肌肉組織之先天性缺陷。氣管支氣管巨大症亦可和馬凡氏症候群,結締組織疾病,毛細血管擴張性運動失調,僵直性脊椎炎,皮膚鬆弛症及輕鏈沉積病等疾病有所關聯。在此,我們報告一個有氣管支氣管巨大症合併僵直性脊椎炎的男性案例。

並列摘要


Tracheobronchomegaly, also called Mounier-Kuhn syndrome, is a distinct condition that involves marked dilation of the trachea and central bronchi, in association with chronic respiratory tract infections. It probably results from a congenital defect of the elastic and muscle fibers within the tracheal and bronchial walls. Secondary tracheobronchomegaly associated with Marfan syndrome, connective tissue diseases, ataxia-telangiectasia, ankylosing spondylitis, cutis laxa, light chain deposition disease, and others, has also been described. In patients with ankylosing spondylitis, the most commonly described pulmonary manifestations are upper lobe fibrosis, mycetoma formation, and pleural thickening. Tracheobronchomegaly is a rare finding in ankylosing spondylitis. We reported a male patient with both tracheobronchomegaly and ankylosing spondylitis.

延伸閱讀