- 期刊
Tuberous Sclerosis Complex-Lymphangioleiomyomatosis Initially Presenting as Acute Abdominal Pain: A Case Report and Literature Review
肺淋巴管平滑肌增生症以不尋常的急性腹痛表現：病例報告
摘要
腹痛在急診室是很常見的問題，在罕見的肺淋巴管平滑肌增生症也可能以腹痛來表現。我們提出一個病患她因為急性腹痛伴隨有休克的症狀被送至急診，經診斷為左側腎臟血管脂肪瘤出血。因為經導管動脈栓塞術止血失敗，病人接受腎臟切除。一年後，病人開始有活動性喘不適的表現。病人肺功能有阻塞性與限制性的混合表現，經過長效ß受體激動劑的治療，病人症狀明顯改善。
並列摘要
Abdominal pain is a common complaint at the emergency room. Rare congenital disorders, like tuberous sclerosis complex-lymphangioleiomyomatosis (TSC-LAM), may initially present as abdominal pain. But, the underlying disease is often neglected. Herein we report a patient with severe acute abdominal pain and hypovolemic shock due to massive bleeding from renal angiomyolipoma. The patient underwent surgical excision of the left kidney after failure of transcatheter arterial embolization. One year post-surgery, the patient developed progressive dyspnea. The initial impression was TSC-LAM, based on clinical manifestations, and imaging and pathology studies. The pulmonary function test revealed mixed restrictive and obstructive ventilatory defects. Her symptoms improved with bronchodilator use.
延伸閱讀
- Yen, P. S., Wan, Y. L., Ng, S. H., Hung, C. F., Tsai, C. C., & Ho, Y. S. (1995). 肺淋巴管平滑肌瘤症：病例報告. 中華放射線醫學雜誌, 20(1), 89-93. https://www.airitilibrary.com/Article/Detail?DocID=10188940-199503-20-1-89-93-a
- Wu, K. M., Sheu, C. Y., Tzen, C. Y., & Chen, P. J. (2002). 肺淋巴管平滑肌增生症：病例報告及文獻回顧. 胸腔醫學, 17(3), 303-308. https://www.airitilibrary.com/Article/Detail?DocID=10239855-200209-17-3-303-308-a
- Liang, H. C., Ho, S. Y., Yeh, K. T., Hsu, N. Y., & Lai, Y. J. (2005). 以下腹部症狀先於肺部症狀的一例淋巴管平滑肌增生症報告. The Changhua Journal of Medicine, 10(3), 158-162. https://www.airitilibrary.com/Article/Detail?DocID=16801504-200507-10-3-158-162-a
- Chen, K. Y., Hsieh, M. J., Lin, M. C., Tsai, Y. H., & Tsao, T. C. (2001). 肺淋巴血管平滑肌增生症以類似支氣管氣喘表現之：病例報告. 胸腔醫學, 16(4), 282-288. https://www.airitilibrary.com/Article/Detail?DocID=10239855-200112-16-4-282-288-a
- Hu, J. T., Yang, S. S., Lai, Y. C., Tai, F. C., & Huang, S. H. (2002). 以急性腹症爲表現的腸系膜血管外皮細胞瘤：一病例報告. 臺灣消化醫學雜誌, 19(4), 257-262. https://doi.org/10.6557/GJT.200212_19(4).0003