Spontaneous Hemothorax Caused by Ruptured Right Subclavian Artery in a Patient with Neurofibromatosis Type 1

神經性纖維瘤病人因右側鎖骨下動脈破裂所引起的自發性血胸－病例報告

尹順盈(Shun-Ying Yin) ； 陳子平(Tzu-Ping Chen) ； 葉集孝(Chi-Hsiao Yeh)

《胸腔醫學》 30卷3期 (2015/06) Pp. 178-182

摘要

自發性血胸是相當罕見但卻對生命造成危急的情況，在臨床上除了胸主動脈瘤破裂或是自發性氣胸因增生迷路血管斷裂會造成自發性血胸外，神經性纖維瘤第一型所引起的血管病變也有可能引起自發性血胸。本文提出一位患有神經性纖維瘤第一型的37歲女性，因右側鎖骨下動脈破裂造成的自發性血胸。我們直接利用手術的方式成功地將血管綁紮止血，而且病人術後恢復良好。現今的治療方式除了手術外還包括了血管栓塞以及血管支架置放；至於哪種方式較好還是要視病人當時的生命徵象來決定。

關鍵字

自發性血胸 ； 神經性纖維瘤

並列摘要

Spontaneous hemothorax is a rare but life-threatening condition. Vascular manifestations of neurofibromatosis type 1 (NF1), or Von Recklinghausen disease, are rare, but may be fatal if they are disrupted. We report the case of a 37-year-old woman with NF1 who developed a spontaneous right massive hemothorax caused by a branch of the right subclavian artery. We successfully performed direct surgical ligation of the bleeding vessel, and the patient's recovery was uneventful. Spontaneous hemothorax in patients with NF1 is a life-threatening condition and may require emergency surgery or endovascular embolization/stenting, depending on the hemodynamic status.

並列關鍵字

spontaneous hemothorax ； neurofibromatosis