Extraskeletal Myxoid Chondrosarcoma of Shoulder Joint-A Case Report and Literature Review

發生於肩關節骨骼外黏液樣軟骨肉瘤－一病例報告及文獻回顧

蔡子斌(Tzyy-Bin Tsay) ； 湯崇彥(Chong-Yan Tang) ； 陳錦時(Jin-Shyr Chen)

《中華民國整形外科醫學會雜誌》 9卷3期 (2000/09) Pp. 182-187

https://doi.org/10.7096/JPSA.200009.0007

摘要

骨骼外黏液樣軟骨肉瘤是一種極少見從軟組織長出的軟骨肉瘤，它有組織上特殊的表徵。大部份文獻報告指出其好發在四肢以及肩胛骨上的位置。其治療方法為外科手術治療，至於是否合併其他輔助性治療，如放射治療或化學治療等並無一定論，有些文獻報告討論依其組織學表徵，是否復發或遠處轉移等，決定是否合併放射治療或化學治療。但絕大多數並無效果。
我們在此報導一發生在右側肩關節骨骼外黏液樣軟骨肉瘤被誤診為創傷後軟組織血腫的病例報告，其術後接受放射治療及化學治療並無效果與文獻報告相同。外科手術仍為第一線選擇。但其術後復發及肺轉移之快速與文獻報告所討論並不相同。

並列摘要

Extraskeletal Myxoid Chondrosarcoma is a rare, soft tissue tumor with a characteristic histologic appearance. Most of the tumors occur in the extremities, and these tumors behave in a less aggressive manner than do other forms of chondrosarcoma. Surgery is the treatment of choice, and adjuvant radiotherapy or chemotherapy should be considered for cases that display a more cellular pattern, a less conspicuous myxoid matrix or distant metastasis happened. To our case, this soft tissue mass is originally misdiagnosed as a hematoma at local hospital, then the patient received the marginal excision and post-operative adjuvant radiotherapy later. But local recurrence and lung metastasis were noted one year later. Chemotherapy was suggested, but the patient refused due to the side effect. In addition, there are no roles of treatment with radiotherapy and chemotherapy, surgery is the first choice. This is the same as the reported literature. The rapid progression with metastasis and recurrence of this case is different from the literature review.

並列關鍵字

extraskeletal myxoid chondrosarcoma