Punctate Porokeratotic Keratoderma (Punctate Porokeratosis): A True Variant of Porokeratosis or A Ner Entity? -Case Report and Literature Review-

點狀汗孔角化角皮症〈點狀汗孔角化症〉：汗孔角化症的變異型抑或新的疾病？─病例報告及文獻回顧─

蔡宗憲(Tsung-Hsien Tsai) ； 莊士迪(Shyh-Dyi Chung) ； 李婉若(Woan-Ruoh Lee)

《中華皮膚科醫學雜誌》 19卷1期 (2001/03) Pp. 75-80

摘要

目前對於點狀汗管角化角皮症或稱點狀汗管角化症究竟是屬於汗管角化症之變異型或是另一截然不同之疾病仍有許多爭議。在本文中，我們報告一例二十五歲男性在其左手手掌分佈許多無症狀角化栓子，組織病理學可見類似玉米狀層〈cornoid lamella〉不全角化柱，下方顆粒層缺失或減少，但角質細胞卻無空泡化或角化不良現象。我們文中藉由文獻回顧嘗試予此疾病作適當之分類。

並列摘要

It is still controversial whether punctuate porokeratotic keratoderma (punctuate porokeratosis) is a variant of porokeratosis or a new entity. We report on a case of a 25-year-old male with peculiar keratotic plugs on his left palm. The histopathologic findings revealed a cornoid lamellar-like column, under which a reduced-to-absent granular layer was noted. No dyskeratosis or vacuolization of keratinocytes was seen. We try to address an appropriate nosologic designation for this entity by reviewing the literature.

並列關鍵字

Punctate porokeratotic keratoderma ； Porokeratosis