An H-type tracheoesophageal fistula (T-E fistula) is a rare congenital abnormality. The diagnosis is made using an esophagogram and/or endoscopy. Early diagnosis of this disorder is still a challenge to pediatricians. Surgical repair is the standard treatment for patients with H-type tracheoesophageal fistulae. Recently, some bronchoscopic procedures have been developed to obliterate the fistulae.