Inflammatory Myofibroblastic Tumor Presenting as Acute Abdomen: Report of One Case

以腹部急症表現之發炎性肌纖維母細胞瘤：一病例報告

溫秀惠(Hsiu-Huei Wen) ； 鄭貴麟(Kui-Lin Cheng) ； 黃耀康(Yau-Kan Huang) ； 張北葉(Pei-Yeh Chang)

《Acta Paediatrica Taiwanica》 48卷6期 (2007/12) Pp. 337-341

https://doi.org/10.7097/APT.200712.0337

摘要

發炎性肌纖維母細胞瘤(IMT)是由紡錘形之肌纖維細胞所組成的種極少見之良性生腫瘤，其原因不明，可發生於任何年齡及任何器官。近年來有越來越多的IMT發生於兒童之病例報告，然而，在台灣此腫瘤發生於兒童腹腔內之病例卻極少見於文獻。我們報告一例此病發生於一歲九個月的男孩，主要症狀爲持續二天的發燒及腹痛，症狀類似腹部急症。經影像學檢查，發現在右側腹部有一近10公分大，來源及性質不明之腫瘤，經手術切除後，病理切片證實爲IMT。根據過去的經驗，IMT要在術前診斷是非常困難的，所以以免疫組織化學染色法做爲病理診斷的基礎變得非常重要。此病例提醒我們在兒童若有不明原因之腹腔內腫瘤併高燒不退時，要考慮到IMT之可能性。

關鍵字

發炎性肌纖維母細胞瘤 ； 腹部急症 ； 腹腔內腫瘤 ； 囊腫

並列摘要

Inflammatory myofibroblastic tumor (IMT) is a very rare benign tumor composed of myojIbroblastic spindle cells of uncertain etiology, which can occur at any age and affect any organ system. More and more cases of IMT in children have been described in pediatric literature in recent years. However, this tumor occurring intraabdominally in children has rarely been reported in Taiwan. Here we present a 1-year-9-month-old boy who had fever and abdominal pain only for 2 days, symptoms mimicking acute abdomen. After imaging study, a huge tumor nearly 10 cm in diameter was incidentally found over the right abdomen with unknown origin and nature. After surgical removal of the tumor, IMT was confirmed by the pathologicalfindings. It is very difficult to make an accurate preoperative diagnosis on this tumor according to past experience, so the role of pathological diagnosis with immunohistochemical study becomes important. This case illustrates that IMT should be considered as a possible cause of intra-abdominal mass in children who have fever of unknown origin.

並列關鍵字

inflammatory myofibroblastic tumor ； acute abdomen ； intra-abdominal mass ； cyst