牙本質發育不全的全口重建治療：病例報告

牙本質發育不全（Dentinogenesis imperfecta, DGI）為一種自體顯性遺傳疾病。本病例報告為一位十二歲的女孩，口內檢查發現多顆牙齒嚴重的磨耗與咬合高度的喪失，恆牙第一大臼齒頰側有膿瘍產生。放射影像顯示多顆牙冠像球莖且牙根短，根管有明顯阻塞的現象。結合家族史及以上檢查結果，診斷為第二型牙本質發育不全。考量該病患的臨床表徵及經濟狀況，治療計畫為拔除預後不良的恆牙第一大臼齒，全口使用不鏽鋼成型牙冠復形，重建咬合高度，上下正中、側門齒與犬齒使用開窗加上複合樹脂填補。牙本質發育不全需要早期診斷治療，並定期追蹤。此病患治療完半年，結果顯示此治療方式可以改善咀嚼功能，重建美觀與信心。未來隨著病患年齡增長，需接受更進一步的贗復及矯正評估治療。

關鍵字

牙本質發育不全；自體顯性遺傳疾病；不鏽鋼成型牙冠

並列摘要

Dentinogenesis imperfecta (DGI) is an autosomal dominant disease. This is a case of a 12-year-old girl, and intraoral examination revealed severe teeth attrition, occlusal vertical dimension loss, and abscess over her buccal side of her first permanent molars. Radiographic image showed multiple teeth exhibiting bulbous crown, short root, and pulpal obliteration. According to the above findings and her family history, the girl was diagnosed with Dentinogenesis imperfecta type II. Taking into consideration of the patient's clinical presentation and economic conditions, the treatment plan was as follows: Extraction of permanent first molars due to poor prognosis, full mouth stainless steel crown reconstruction, central, lateral incisor and canine restoration using open-faced stainless steel crowns to rehabilitate esthetics and function. Early diagnosis, treatment, and regular follow-up of DGI are recommended. At 6-months follow-up, the results show that this treatment can improve chewing function, aesthetics and rebuild confidence. In the future, a further treatment and evaluation of multidisciplinary approach is imperative.

並列關鍵字

Dentinogenesis Imperfecta ； Inherent Autosomal Dominant ； Stainless Steel Crowns

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牙本質發育不全的全口重建治療：病例報告

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