Rehabilitation of a Child with Type II Dentinogenesis Imperfecta: A Case Report

第二類型牙本質發育不全的全口重建：病例報告

黃于倩(Yu-Chien Huang) ； 詹嘉一(Chia-Yi Jan)

《臺灣兒童牙醫學雜誌》 17卷4期 (2017/12) Pp. 161-165

https://doi.org/10.6319/TJPD.2017.17(4).0005

摘要

Dentinogenesis imperfecta, an autosomal dominant disease, is one of the most common hereditary abnormality of dentin formation. Full mouth rehabilitation of those cases represents a challenge for dental practitioners. A case is reported as a 4-year-old boy came with severe teeth attrition and vertical dimension loss. Intraoral examination revealed that the dentition was attrited to the middle and cervical third of teeth with pale greyish enamel and amber dentine. Radiographically, the crowns were bulbous with cervical constriction and the root canals showed obliteration. According to the family history, his father and grandfather were both in the same situation. In addition of no history of osteogenesis imperfecta, our diagnosis was type II dentinogenesis imperfecta. The treatment was done for retrieving the vertical dimension, and the esthetic appearance of teeth. Periodically preventive care is needed.

關鍵字

Dentinogenesis imperfecta ； tooth attrition ； removable partial denture ； stainless steel crown

並列摘要

牙本質發育不全（dentinogenesis imperfecta）是常遇到的自體顯性遺傳疾病之一，當遇到需要全口重建的病例更是一大挑戰，此篇呈現的病例是一個四歲的小男生，主訴是覺得牙齒磨耗嚴重影響進食效率，口內檢查全口牙齒平均磨耗到牙齒頸部三分之一，且牙釉質灰白牙本質呈現琥珀色，根尖片顯示球莖狀牙冠且根管細窄，加上患者的爸爸及爺爺都有此症狀，診斷為第二型牙本質發育不全，治療目的為恢復咬合高度及增進前牙美觀，並且定期追蹤保健。

並列關鍵字

牙本質發育不全 ； 牙齒磨耗 ； 活動假牙 ； 不鏽鋼成型牙冠