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A Case Report of a Female Patient Who Presented a Hepatic Mesenchymal Hamartoma that Grew Since Childhood
自幼發現之實質樣肝臟間葉缺陷瘤：一個成年女性之罕見個案報告
摘要
Hepatic mesenchymal hamartoma (HMH) is commonly observed in pediatric patients aged below 2 years, and it accounts for about 3%-8% of all primary liver tumors in children. HMH usually presents as a cystic tumor with multiple septa and variable solid components. However, the whole tumor may sometimes appear as a solid mass. This type of tumor is rarely observed in adults, and only about 46 adult cases were reported. Herein, we discuss the case of a 23-year-old woman diagnosed with HMH at the age of 5 years via surgical biopsy. Because the tumor could not be resected at that time, liver transplantation was recommended. However, the parents refused to let their child undergo the procedure. Several years after the initial diagnosis, the patient did not receive any management for her HMH, and she only sought treatment after recently experiencing progressive abdominal discomfort. Thus, da Vinci robotic-assisted central hepatectomy with total tumor excision was performed.
並列摘要
肝臟間葉缺陷瘤（HMH）通常發生在2歲以下的小兒病患。它們佔所有小兒原發性肝腫瘤的百分之三～八。肝臟間葉缺陷瘤通常表現為具有多個隔膜和多樣實質構造所組成的囊狀腫瘤。少數肝臟間葉缺陷瘤可能表現為實質狀腫塊。肝臟間葉缺陷瘤在成人中發現的案例很少。目前僅報告46例成人病例。在本報告中，我們討論了一名23歲的女性案例，她在5歲時經由手術活檢診斷出患有肝臟間葉缺陷瘤。由於當時的技術無法安全切除整個腫瘤，於是建議進行肝臟移植，但病患父母當時拒絕了肝臟移植這項手術。在診斷後的這十幾年間，患者沒有再接受過任何有關她肝臟間葉缺陷瘤的治療。最近由於患者逐漸感到腹部不適後才又尋求治療。在本院她接受了達文西機器手臂輔助的中央肝臟切除手術，順利將整個腫瘤切除。